Ortho Free Review | Dr Hutaif General Orthopedics Revie -...

DISCUSSION: The clinical description is of a patient with neurofibromatosis, NF-1. Although most of the
hoices can occur with NF-1 or sequelae of secondary malignancy, the new onset of cardiac symptoms should prompt an urgent cardiology evaluation for aortic stenosis, which occurs in approximately 2% of cases. Superior mesenteric syndrome is a rare complication after scoliosis surgery but could not be a source of lethargy prior to scoliosis surgery. Lisch nodules are neurofibromas of the iris and are not an urgent problem at this time. Acute chest syndrome occurs most commonly in patients with sickle cell anemia and would not be typical of patients with NF-1. The Preferred Response to Question # 40 is 1.